

Propinol-L-Carnitine
$89.25 – $141.75
Size |
10mg ,50mg |
---|
CAS #
20064-19-1
Concentration
98.00%
Description
Propinol-L-Carnitine is present in high abundance in the urine of patients with Methylmalonyl-CoA mutase (MUT) deficiency, together with Methylmalonic acid. MUT is a mitochondrial enzyme that catalyzes the isomerization of methylmalonyl-CoA to succinyl-CoA.
Keywords
(2R)-3-Carboxy-N,N,N-trimethyl-2-(1-oxopropoxy)-1-propanaminium inner salt, L-Carnitine propionyl ester, C3-Carnitine, Propanoyl-L-carnitine
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